| Approved Symbol | Approved Name | Previous Symbols | Aliases | Chromosome | Accession Numbers | RefSeq IDs |
| DEFA1 | defensin, alpha 1 | DEF1, MRS, DEFA2 | HNP-1 | 8p23.1 | M26602 | NM_004084 |
| DEFA1A3 | defensin, alpha 1 and alpha 3, variable copy number locus | | DEFA1, DEFA3, DEFT1P | 8p23.1 | | |
| DEFA3 | defensin, alpha 3, neutrophil-specific | DEF3 | HNP-3 | 8p23.1 | M23281 | NM_005217 |
| DEFA4 | defensin, alpha 4, corticostatin | DEF4 | HP-4 | 8p23.1 | X65977 | NM_001925 |
| DEFA5 | defensin, alpha 5, Paneth cell-specific | DEF5 | HD-5 | 8p23.1 | BC069690 | NM_021010 |
| DEFA6 | defensin, alpha 6, Paneth cell-specific | | HD-6, DEF6 | 8p23.1 | M98331 | NM_001926 |
| DEFA7P | defensin, alpha 7 pseudogene | DEFA7 | | 8p23.1 | AY746432 | |
| DEFA8P | defensin, alpha 8 pseudogene | | DEFAP1 | 8p23.1 | AY746433 | |
| DEFA9P | defensin, alpha 9 pseudogene | | DEFAP2 | 8p23.1 | AY746434 | |
| DEFA10P | defensin, alpha 10 pseudogene | | | 8p23.1 | AY746435 | |
| DEFA11P | defensin, alpha 11 pseudogene | | DEFAP3 | 8p23.1 | AY746436 | |