Homeoboxes
External resources:
Homeodomain Resource NHGRI
Holland PW, Booth HA, Bruford EA. Classification and nomenclature of all human homeobox genes. BMC Biol. 2007 Oct 26;5:47. PMID:17963489
Click on the Approved Gene Symbol to retrieve the complete gene record
ANTP class homeoboxes: HOXL subclass homeoboxes
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| HOXA1 | homeobox A1 | HOX1F, HOX1 | 7p15.2 | |
| HOXA2 | homeobox A2 | HOX1K | 7p15.2 | |
| HOXA3 | homeobox A3 | HOX1E, HOX1 | 7p15.2 | |
| HOXA4 | homeobox A4 | HOX1D, HOX1 | 7p15.2 | |
| HOXA5 | homeobox A5 | HOX1C, HOX1 | 7p15.2 | |
| HOXA6 | homeobox A6 | HOX1B, HOX1 | 7p15.2 | |
| HOXA7 | homeobox A7 | HOX1A, HOX1 | 7p15.2 | |
| HOXA9 | homeobox A9 | HOX1G, HOX1 | 7p15.2 | |
| HOXA10 | homeobox A10 | HOX1H, HOX1 | 7p15.2 | |
| HOXA11 | homeobox A11 | HOX1I, HOX1 | 7p15.2 | |
| HOXA13 | homeobox A13 | HOX1J, HOX1 | 7p15.2 | |
| HOXB1 | homeobox B1 | HOX2, HOX2I | 17q21.32 | |
| HOXB2 | homeobox B2 | HOX2, HOX2H | 17q21.32 | |
| HOXB3 | homeobox B3 | HOX2, HOX2G | 17q21.32 | |
| HOXB4 | homeobox B4 | HOX2, HOX2F | 17q21.32 | |
| HOXB5 | homeobox B5 | HOX2, HOX2A | 17q21.32 | |
| HOXB6 | homeobox B6 | HOX2, HOX2B | 17q21.32 | |
| HOXB7 | homeobox B7 | HOX2, HOX2C | 17q21.32 | |
| HOXB8 | homeobox B8 | HOX2, HOX2D | 17q21.32 | |
| HOXB9 | homeobox B9 | HOX2E, HOX2 | 17q21.32 | |
| HOXB13 | homeobox B13 | 17q21.32 | ||
| HOXC4 | homeobox C4 | HOX3, HOX3E | 12q13.13 | |
| HOXC5 | homeobox C5 | HOX3D, HOX3 | 12q13.13 | |
| HOXC6 | homeobox C6 | HOX3C, HOX3 | 12q13.13 | |
| HOXC8 | homeobox C8 | HOX3, HOX3A | 12q13.13 | |
| HOXC9 | homeobox C9 | HOX3, HOX3B | 12q13.13 | |
| HOXC10 | homeobox C10 | HOX3I | 12q13.13 | |
| HOXC11 | homeobox C11 | HOX3H | 12q13.13 | |
| HOXC12 | homeobox C12 | HOX3, HOX3F, HOC3F | 12q13.13 | |
| HOXC13 | homeobox C13 | HOX3, HOX3G | 12q13.13 | |
| HOXD1 | homeobox D1 | HOX4, HOX4G | 2q31.1 | |
| HOXD3 | homeobox D3 | HOX4A, HOX4, HOX1D | 2q31.1 | |
| HOXD4 | homeobox D4 | HOX4B, HOX4 | 2q31.1 | |
| HOXD8 | homeobox D8 | HOX4, HOX4E | 2q31.1 | |
| HOXD9 | homeobox D9 | HOX4C, HOX4 | 2q31.1 | |
| HOXD10 | homeobox D10 | HOX4, HOX4D | 2q31.1 | |
| HOXD11 | homeobox D11 | HOX4, HOX4F | 2q31.1 | |
| HOXD12 | homeobox D12 | HOX4H | 2q31.1 | |
| HOXD13 | homeobox D13 | HOX4I, SPD | 2q31.1 | |
| CDX1 | caudal type homeobox 1 | 5q32 | ||
| CDX2 | caudal type homeobox 2 | CDX3 | 13q12.2 | |
| CDX4 | caudal type homeobox 4 | Xq13.2 | ||
| EVX1 | even-skipped homeobox 1 | 7p15.2 | ||
| EVX2 | even-skipped homeobox 2 | 2q31.1 | ||
| GBX1 | gastrulation brain homeobox 1 | 7q36.1 | ||
| GBX2 | gastrulation brain homeobox 2 | 2q37.2 | ||
| GSX1 | GS homeobox 1 | GSH1 | Gsh-1 | 13q12.2 |
| GSX2 | GS homeobox 2 | Gsh2 | 4q12 | |
| MEOX1 | mesenchyme homeobox 1 | MOX1 | 17q21.31 | |
| MEOX2 | mesenchyme homeobox 2 | GAX | MOX2 | 7p22.1-p21.3 |
| MNX1 | motor neuron and pancreas homeobox 1 | HLXB9 | HB9, HOXHB9, SCRA1 | 7q36 |
| PDX1 | pancreatic and duodenal homeobox 1 | IPF1 | IDX-1, STF-1, PDX-1, MODY4 | 13q12.1 |
ANTP class homeoboxes: NKL subclass homeoboxes and pseudogenes
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| NKX1-1 | NK1 homeobox 1 | HSPX153, SAX2 | 4p16.3 | |
| NKX1-2 | NK1 homeobox 2 | C10orf121 | bB238F13.2 | 10q26.13 |
| NKX2-1 | NK2 homeobox 1 | NKX2A, BCH, TITF1 | TTF-1, TTF1 | 14q13.3 |
| NKX2-2 | NK2 homeobox 2 | NKX2B | NKX2.2 | 20p11.22 |
| NKX2-3 | NK2 homeobox 3 | NKX2C | NKX2.3, CSX3, NKX4-3 | 10 |
| NKX2-4 | NK2 homeobox 4 | NKX2D | NKX2.4 | 20p11.22 |
| NKX2-5 | NK2 homeobox 5 | CSX, NKX2E | CSX1, NKX2.5, NKX4-1 | 5q34 |
| NKX2-6 | NK2 homeobox 6 | CSX2, NKX4-2 | 8p21.2 | |
| NKX2-8 | NK2 homeobox 8 | NKX2H | NKX2.8, Nkx2-9 | 14q13.3 |
| NKX3-1 | NK3 homeobox 1 | NKX3A | NKX3.1, BAPX2 | 8p21.2 |
| NKX3-2 | NK3 homeobox 2 | BAPX1 | NKX3B, NKX3.2 | 4p16.3 |
| NKX6-1 | NK6 homeobox 1 | NKX6A | Nkx6.1 | 4q21.33 |
| NKX6-2 | NK6 homeobox 2 | NKX6B, GTX, NKX6.1 | 10q26.3 | |
| NKX6-3 | NK6 homeobox 3 | FLJ25169 | 8p11.21 | |
| BARHL1 | BarH-like homeobox 1 | 9q34.13 | ||
| BARHL2 | BarH-like homeobox 2 | 1p22.2 | ||
| BARX1 | BARX homeobox 1 | 9q22.32 | ||
| BARX2 | BARX homeobox 2 | 11q24.3 | ||
| BSX | brain-specific homeobox | BSX1 | 11q24.1 | |
| DBX1 | developing brain homeobox 1 | 11p15.1 | ||
| DBX2 | developing brain homeobox 2 | FLJ16139 | 12q12 | |
| DLX1 | distal-less homeobox 1 | 2q31.1 | ||
| DLX2 | distal-less homeobox 2 | TES-1 | 2q31.1 | |
| DLX3 | distal-less homeobox 3 | 17q21.33 | ||
| DLX4 | distal-less homeobox 4 | DLX7, DLX9 | DLX8, BP1 | 17q21.33 |
| DLX5 | distal-less homeobox 5 | 7q21.3 | ||
| DLX6 | distal-less homeobox 6 | 7q21.3 | ||
| EMX1 | empty spiracles homeobox 1 | 2p13.2 | ||
| EMX2 | empty spiracles homeobox 2 | 10q26.11 | ||
| EN1 | engrailed homeobox 1 | 2q14.2 | ||
| EN2 | engrailed homeobox 2 | 7q36.2 | ||
| HHEX | hematopoietically expressed homeobox | PRHX | HEX, HOX11L-PEN | 10q23.33 |
| HLX | H2.0-like homeobox | HLX1 | HB24 | 1q41 |
| HMX1 | H6 family homeobox 1 | H6, NKX5-3 | 4p16.1 | |
| HMX2 | H6 family homeobox 2 | NKX5-2 | 10q26.13 | |
| HMX3 | H6 family homeobox 3 | NKX5-1 | 10q26.13 | |
| LBX1 | ladybird homeobox 1 | LBX1H, HPX6 | 10q24.32 | |
| LBX2 | ladybird homeobox 2 | 2p13.1 | ||
| MSX1 | msh homeobox 1 | HOX7 | HYD1, OFC5 | 4p16.2 |
| MSX2 | msh homeobox 2 | PFM1 | CRS2, FPP, HOX8, MSH, PFM | 5q35.2 |
| MSX2P1 | msh homeobox 2 pseudogene 1 | MSX2P | HSHPX5, HPX5 | 17q23.2 |
| NANOG | Nanog homeobox | FLJ12581, FLJ40451 | 12p13.31 | |
| NANOGP1 | Nanog homeobox pseudogene 1 | NANOG2 | 12p13.31 | |
| NANOGP2 | Nanog homeobox pseudogene 2 | NANOGP4 | 2q36.1 | |
| NANOGP3 | Nanog homeobox pseudogene 3 | 6p12.1 | ||
| NANOGP4 | Nanog homeobox pseudogene 4 | NANOGP2 | 7p15.3 | |
| NANOGP5 | Nanog homeobox pseudogene 5 | 9q31.1 | ||
| NANOGP6 | Nanog homeobox pseudogene 6 | 10q24.2 | ||
| NANOGP7 | Nanog homeobox pseudogene 7 | NANOGP3 | 14q32.12 | |
| NANOGP8 | Nanog homeobox pseudogene 8 | 15q13.3 | ||
| NANOGP9 | Nanog homeobox pseudogene 9 | Xq12 | ||
| NANOGP10 | Nanog homeobox pseudogene 10 | Xp11.4 | ||
| NANOGP11 | Nanog homeobox pseudogene 11 | 6q25 | ||
| NOTO | notochord homeobox | 2p13.2 | ||
| TLX1 | T-cell leukemia homeobox 1 | TCL3, HOX11 | 10q24.32 | |
| TLX2 | T-cell leukemia homeobox 2 | HOX11L1 | Enx, Tlx2, NCX | 2p13.1 |
| TLX3 | T-cell leukemia homeobox 3 | HOX11L2 | RNX | 5q35.1 |
| VAX1 | ventral anterior homeobox 1 | 10q26.11 | ||
| VAX2 | ventral anterior homeobox 2 | DRES93 | 2p13.3 | |
| VENTX | VENT homeobox | VENTX2 | HPX42B | 10q26.3 |
| VENTXP1 | VENT homeobox pseudogene 1 | NA88A, CT18 | Xp21.3 | |
| VENTXP2 | VENT homeobox pseudogene 2 | 13q31.1 | ||
| VENTXP3 | VENT homeobox pseudogene 3 | 12q21.1 | ||
| VENTXP4 | VENT homeobox pseudogene 4 | 3p24.2 | ||
| VENTXP5 | VENT homeobox pseudogene 5 | 8p12 | ||
| VENTXP6 | VENT homeobox pseudogene 6 | 8q21.11 | ||
| VENTXP7 | VENT homeobox pseudogene 7 | VENTX1 | HPX42 | 3p24.3 |
PRD class homeoboxes and pseudogenes:
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| ALX1 | ALX homeobox 1 | CART1 | 12q21.31 | |
| ALX3 | ALX homeobox 3 | 1p13.3 | ||
| ALX4 | ALX homeobox 4 | PFM2 | FPP, PFM, KIAA1788 | 11p11.2 |
| ARGFX | arginine-fifty homeobox | 3q13.33 | ||
| ARGFXP1 | arginine-fifty homeobox pseudogene 1 | 5q23.2 | ||
| ARGFXP2 | arginine-fifty homeobox pseudogene 2 | 17q11.2 | ||
| ARX | aristaless related homeobox | MRXS1, PRTS, MRX76, MRX54, MRX43, MRX36, MRX29, MRX32, MRX33, MRX38, MRX87 | ISSX, CT121, EIEE1 | Xp21.3 |
| CRX | cone-rod homeobox | CORD2 | CRD, LCA7, OTX3 | 19q13.3 |
| DMBX1 | diencephalon/mesencephalon homeobox 1 | OTX3 | PAXB | 1p34.1 |
| DPRX | divergent-paired related homeobox | 19q13.42 | ||
| DPRXP1 | divergent-paired related homeobox pseudogene 1 | 2q32.1 | ||
| DPRXP2 | divergent-paired related homeobox pseudogene 2 | 6p21.31 | ||
| DPRXP3 | divergent-paired related homeobox pseudogene 3 | 14q13.2 | ||
| DPRXP4 | divergent-paired related homeobox pseudogene 4 | 17q11.2 | ||
| DPRXP5 | divergent-paired related homeobox pseudogene 5 | 21q22.13 | ||
| DPRXP6 | divergent-paired related homeobox pseudogene 6 | Xp11.4 | ||
| DPRXP7 | divergent-paired related homeobox pseudogene 7 | Xq23 | ||
| DRGX | dorsal root ganglia homeobox | PRRXL1 | DRG11 | 10q11.23 |
| DUX4 | double homeobox 4 | 4q35.2 | ||
| DUX4L2 | double homeobox 4 like 2 | 4q35.2 | ||
| DUX4L3 | double homeobox 4 like 3 | 4q35.2 | ||
| DUX4L4 | double homeobox 4 like 4 | 4q35.2 | ||
| DUX4L5 | double homeobox 4 like 5 | 4q35.2 | ||
| DUX4L6 | double homeobox 4 like 6 | 4q35.2 | ||
| DUX4L7 | double homeobox 4 like 7 | 4q35.2 | ||
| DUX4L8 | double homeobox 4 like 8 (pseudogene) | 4q35.2 | ||
| DUX4L9 | double homeobox 4 like 9 | 4q35.2 | ||
| DUX4L10 | double homeobox 4 like 10 | DUX10 | 10q26.3 | |
| DUX4L11 | double homeobox 4 like 11 | 10q26.3 | ||
| DUX4L12 | double homeobox 4 like 12 | 10q26.3 | ||
| DUX4L13 | double homeobox 4 like 13 | 10q26.3 | ||
| DUX4L14 | double homeobox 4 like 14 | 10q26.3 | ||
| DUX4L15 | double homeobox 4 like 15 | 10q26.3 | ||
| DUX4L16 | double homeobox 4 like 16 | DUXY1 | Yq11.21 | |
| DUX4L17 | double homeobox 4 like 17 | DUXY3 | Yq11.21 | |
| DUX4L18 | double homeobox 4 like 18 | DUXY2 | Yq11.21 | |
| DUX4L19 | double homeobox 4 like 19 | DUXY4 | Yq11.21 | |
| DUXA | double homeobox A | 19q13.43 | ||
| DUXAP1 | double homeobox A pseudogene 1 | 2p11.2 | ||
| DUXAP2 | double homeobox A pseudogene 2 | 8q22.3 | ||
| DUXAP3 | double homeobox A pseudogene 3 | 10q11.21 | ||
| DUXAP4 | double homeobox A pseudogene 4 | 10q11.21 | ||
| DUXAP5 | double homeobox A pseudogene 5 | 11q23.3 | ||
| DUXAP6 | double homeobox A pseudogene 6 | 15q26.1 | ||
| DUXAP7 | double homeobox A pseudogene 7 | 20p11.23 | ||
| DUXAP8 | double homeobox A pseudogene 8 | 22q11.21 | ||
| DUXAP9 | double homeobox A pseudogene 9 | 14q11.2 | ||
| DUXAP10 | double homeobox A pseudogene 10 | 14q11.2 | ||
| DUXB | double homeobox B | 16q23.1 | ||
| ESX1 | ESX homeobox 1 | ESX1L | ESXR1 | Xq22.2 |
| GSC | goosecoid homeobox | 14q32.13 | ||
| GSC2 | goosecoid homeobox 2 | GSCL | 22q11.21 | |
| HESX1 | HESX homeobox 1 | RPX, ANF | 3p14.3 | |
| HOPX | HOP homeobox | LAGY, HOP, OB1, NECC1, SMAP31 | 4q12 | |
| ISX | intestine-specific homeobox | RAXLX | 22q12.3 | |
| LEUTX | leucine twenty homeobox | 19q13.2 | ||
| MIXL1 | Mix paired-like homeobox | MILD1, MIXL | 1q42.12 | |
| NOBOX | NOBOX oogenesis homeobox | OG2, Og2x | 7q35 | |
| OTP | orthopedia homeobox | 5q14.1 | ||
| OTX1 | orthodenticle homeobox 1 | 2p15 | ||
| OTX2 | orthodenticle homeobox 2 | 14q22.3 | ||
| OTX2P1 | orthodenticle homeobox 2 pseudogene 1 | OTX2P | 9q21 | |
| PAX2 | paired box 2 | 10q24.31 | ||
| PAX3 | paired box 3 | WS1 | HUP2 | 2q36.1 |
| PAX4 | paired box 4 | MODY9 | 7q32.1 | |
| PAX5 | paired box 5 | BSAP | 9p13.2 | |
| PAX6 | paired box 6 | AN2 | D11S812E, AN, WAGR | 11p13 |
| PAX7 | paired box 7 | Hup1 | 1p36.13 | |
| PAX8 | paired box 8 | 2q13 | ||
| PHOX2A | paired-like homeobox 2a | ARIX, FEOM2 | PMX2A, CFEOM2 | 11q13.4 |
| PHOX2B | paired-like homeobox 2b | PMX2B | Phox2b, NBPhox | 4p13 |
| PITX1 | paired-like homeodomain 1 | BFT | PTX1, POTX | 5q31.1 |
| PITX2 | paired-like homeodomain 2 | IRID2, IHG2, RIEG, RIEG1, RGS | IGDS, RS, Brx1, Otlx2, ARP1 | 4q25 |
| PITX3 | paired-like homeodomain 3 | 10q24.32 | ||
| PROP1 | PROP paired-like homeobox 1 | 5q35.3 | ||
| PRRX1 | paired related homeobox 1 | PMX1 | PHOX1 | 1q24.3 |
| PRRX2 | paired related homeobox 2 | PRX2, PMX2 | 9q34.11 | |
| RAX | retina and anterior neural fold homeobox | RX | 18q21.31 | |
| RAX2 | retina and anterior neural fold homeobox 2 | RAXL1 | MGC15631, ARMD6 | 19p13.3 |
| RHOXF1 | Rhox homeobox family, member 1 | OTEX, PEPP1 | Xq24 | |
| RHOXF2 | Rhox homeobox family, member 2 | THG1, PEPP-2, PEPP2, CT107 | Xq24 | |
| RHOXF2B | Rhox homeobox family, member 2B | Xq24 | ||
| SEBOX | SEBOX homeobox | OG9, OG9X | 17q11.2 | |
| SHOX | short stature homeobox | PHOG, GCFX, SS, SHOXY | Xp22.33 and Yp11.32 | |
| SHOX2 | short stature homeobox 2 | SHOT, OG12X, OG12 | 3q25.32 | |
| TPRX1 | tetra-peptide repeat homeobox 1 | FLJ40321 | 19q13.33 | |
| TPRX1P1 | tetra-peptide repeat homeobox 1 pseudogene 1 | 10q22.3 | ||
| TPRX2P | tetra-peptide repeat homeobox 2 pseudogene | TPRX2P1 | 19q13.32 | |
| TPRXL | tetra-peptide repeat homeobox-like | FLJ35107 | 3p25.1 | |
| UNCX | UNC homeobox | Uncx4.1 | 7p22.3 | |
| VSX1 | visual system homeobox 1 | PPCD | PPD | 20p11.21 |
| VSX2 | visual system homeobox 2 | HOX10, CHX10 | RET1 | 14q24.3 |
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| LHX1 | LIM homeobox 1 | LIM-1, LIM1 | 17q12 | |
| LHX2 | LIM homeobox 2 | LH-2, hLhx2 | 9q33.3 | |
| LHX3 | LIM homeobox 3 | 9q34.3 | ||
| LHX4 | LIM homeobox 4 | Gsh4 | 1q25.3 | |
| LHX5 | LIM homeobox 5 | 12q24.13 | ||
| LHX6 | LIM homeobox 6 | LHX6.1 | 9q33.2 | |
| LHX8 | LIM homeobox 8 | Lhx7 | 1p31.1 | |
| LHX9 | LIM homeobox 9 | 1q31.1 | ||
| LMX1A | LIM homeobox transcription factor 1, alpha | LMX1 | LMX1.1 | 1q24.1 |
| LMX1B | LIM homeobox transcription factor 1, beta | NPS1 | 9q33.3 | |
| ISL1 | ISL LIM homeobox 1 | Isl-1, ISLET1 | 5q11.2 | |
| ISL2 | ISL LIM homeobox 2 | FLJ10160 | 15q24.3 |
POU class homeoboxes and pseudogenes:
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| POU1F1 | POU class 1 homeobox 1 | PIT1 | GHF-1, POU1F1a | 3p11.2 |
| POU2F1 | POU class 2 homeobox 1 | OTF1 | OCT1 | 1q24.2 |
| POU2F2 | POU class 2 homeobox 2 | OTF2 | OCT2 | 19q13.2 |
| POU2F3 | POU class 2 homeobox 3 | OCT11, PLA-1, Skn-1a, Epoc-1 | 11q23.3 | |
| POU3F1 | POU class 3 homeobox 1 | OTF6 | OCT6, SCIP | 1p34.3 |
| POU3F2 | POU class 3 homeobox 2 | OTF7 | POUF3, BRN2, OCT7 | 6q16.2 |
| POU3F3 | POU class 3 homeobox 3 | BRN1, OTF8 | 2q12.1 | |
| POU3F4 | POU class 3 homeobox 4 | DFN3 | BRN4, OTF9, DFNX2 | Xq21.1 |
| POU4F1 | POU class 4 homeobox 1 | BRN3A | RDC-1 | 13q31.1 |
| POU4F2 | POU class 4 homeobox 2 | BRN3B | Brn-3b | 4q31.22 |
| POU4F3 | POU class 4 homeobox 3 | DFNA15 | BRN3C | 5q32 |
| POU5F1 | POU class 5 homeobox 1 | OTF3 | OCT3, Oct4, MGC22487 | 6p21.33 |
| POU5F1B | POU class 5 homeobox 1B | OTF3P1, POU5F1P1 | OTF3C | 8q24.21 |
| POU5F1P2 | POU class 5 homeobox 1 pseudogene 2 | 8q22.3 | ||
| POU5F1P3 | POU class 5 homeobox 1 pseudogene 3 | OTF3L, POU5F1L | POU5FLC12 | 12p13.31 |
| POU5F1P4 | POU class 5 homeobox 1 pseudogene 4 | POU5FLC1 | 1q22 | |
| POU5F1P5 | POU class 5 homeobox 1 pseudogene 5 | 10q21.3 | ||
| POU5F1P6 | POU class 5 homeobox 1 pseudogene 6 | 3q21.3 | ||
| POU5F1P7 | POU class 5 homeobox 1 pseudogene 7 | 3q12.1 | ||
| POU5F1P8 | POU class 5 homeobox 1 pseudogene 8 | 17q25.3 | ||
| POU5F2 | POU domain class 5, transcription factor 2 | SPRM-1, FLJ25680 | 5q15 | |
| POU6F1 | POU class 6 homeobox 1 | BRN5, MPOU, TCFB1 | 12q13.13 | |
| POU6F2 | POU class 6 homeobox 2 | RPF-1 | 7p14.1 | |
| HDX | highly divergent homeobox | CXorf43 | FLJ30678 | Xq21.1 |
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| HNF1A | HNF1 homeobox A | MODY3, TCF1 | HNF1, LFB1 | 12q24.31 |
| HNF1B | HNF1 homeobox B | TCF2 | LFB3, VHNF1, HNF1beta, MODY5 | 17q12 |
| HMBOX1 | homeobox containing 1 | HNF1LA, PBHNF, FLJ21616 | 8p12 |
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| SIX1 | SIX homeobox 1 | DFNA23 | 14q23.1 | |
| SIX2 | SIX homeobox 2 | 2p21 | ||
| SIX3 | SIX homeobox 3 | HPE2 | 2p21 | |
| SIX4 | SIX homeobox 4 | AREC3 | 14q23.1 | |
| SIX5 | SIX homeobox 5 | DMAHP | 19q13.32 | |
| SIX6 | SIX homeobox 6 | OPTX2 | Six9 | 14q23.1 |
TALE class homeboxes and pseudogenes:
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| IRX1 | iroquois homeobox 1 | IRX-5 | 5p15.33 | |
| IRX1P1 | iroquois homeobox 1 pseudogene 1 | 13q12.12 | ||
| IRX2 | iroquois homeobox 2 | 5p15.33 | ||
| IRX3 | iroquois homeobox 3 | IRX-1 | 16q12.2 | |
| IRX4 | iroquois homeobox 4 | 5p15.33 | ||
| IRX4P1 | iroquois homeobox 4 pseudogene 1 | 18p11.22 | ||
| IRX5 | iroquois homeobox 5 | IRX-2a | 16q12.2 | |
| IRX6 | iroquois homeobox 6 | IRX7 | IRX-3 | 16q12.2 |
| MEIS1 | Meis homeobox 1 | 2p14 | ||
| MEIS2 | Meis homeobox 2 | MRG1, HsT18361 | 15q14 | |
| MEIS3 | Meis homeobox 3 | MRG2, DKFZp547H236 | 19q13.32 | |
| MEIS3P1 | Meis homeobox 3 pseudogene 1 | MEIS3, MEIS4 | MRG2 | 17p12 |
| MEIS3P2 | Meis homeobox 3 pseudogene 2 | 17p11.2 | ||
| MKX | mohawk homeobox | C10orf48, IRXL1 | MGC39616 | 10p12.1 |
| PBX1 | pre-B-cell leukemia homeobox 1 | 1q23.3 | ||
| PBX2 | pre-B-cell leukemia homeobox 2 | G17, HOX12, PBX2MHC | 6p21.32 | |
| PBX2P1 | pre-B-cell leukemia homeobox 2 pseudogene 1 | PBX2, PBXP1 | 3q24 | |
| PBX3 | pre-B-cell leukemia homeobox 3 | 9q33.3 | ||
| PBX4 | pre-B-cell leukemia homeobox 4 | 19p12 | ||
| PKNOX1 | PBX/knotted 1 homeobox 1 | PREP1 | 21q22.3 | |
| PKNOX2 | PBX/knotted 1 homeobox 2 | 11q24.2 | ||
| TGIF1 | TGFB-induced factor homeobox 1 | HPE4, TGIF | 18p11.31 | |
| TGIF1P1 | TGFB-induced factor homeobox 1 pseudogene 1 | 19q13.32 | ||
| TGIF2 | TGFB-induced factor homeobox 2 | 20q11.23 | ||
| TGIF2LX | TGFB-induced factor homeobox 2-like, X-linked | Xq21.31 | ||
| TGIF2LY | TGFB-induced factor homeobox 2-like, Y-linked | Yp11.2 | ||
| TGIF2P1 | TGFB-induced factor homeobox 2 pseudogene 1 | 1q44 | ||
| TGIF2P2 | TGFB-induced factor homeobox 2 pseudogene 2 | 15q21.1 | ||
| TGIF2P3 | TGFB-induced factor homeobox 2 pseudogene 3 | 15q21.1 | ||
| TGIF2P4 | TGFB-induced factor homeobox 2 pseudogene 4 | 14q24.2 |
CUT class homeoboxes and pseudogenes:
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| ONECUT1 | one cut homeobox 1 | HNF6, HNF6A | HNF-6 | 15q21.3 |
| ONECUT2 | one cut homeobox 2 | OC-2 | 18q21.31 | |
| ONECUT3 | one cut homeobox 3 | 19p13.3 | ||
| CUX1 | cut-like homeobox 1 | CUTL1 | CDP, CDP1, CUX, CUT, Clox, CDP/Cut, CDP/Cux, Cux/CDP, CASP, GOLIM6 | 7q22.1 |
| CUX2 | cut-like homeobox 2 | CUTL2 | KIAA0293, CDP2 | 12q24.12 |
| CUX2P1 | cut-like homeobox 2 pseudogene 1 | 10p14 | ||
| CUX2P2 | cut-like homeobox 2 pseudogene 2 | 4q32.1 | ||
| SATB1 | SATB homeobox 1 | 3p24.3 | ||
| SATB1P1 | SATB homeobox 1 pseudogene 1 | 6q22.31 | ||
| SATB2 | SATB homeobox 2 | KIAA1034, FLJ21474 | 2q33.1 |
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| PROX1 | prospero homeobox 1 | 1q41 | ||
| PROX2 | prospero homeobox 2 | FLJ36749 | 14q24.3 |
ZF class homeoboxes and pseudogenes:
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| ZFHX2 | zinc finger homeobox 2 | ZNF409 | KIAA1762, KIAA1056, ZFH-5 | 14q11.2 |
| ZFHX3 | zinc finger homeobox 3 | ATBF1 | ZNF927 | 16q22.3 |
| ZFHX4 | zinc finger homeobox 4 | ZFH4, FLJ20980 | 8q21.11 | |
| ZHX1 | zinc fingers and homeoboxes 1 | 8q24.13 | ||
| ZHX2 | zinc fingers and homeoboxes 2 | KIAA0854 | 8q24.13 | |
| ZHX3 | zinc fingers and homeoboxes 3 | TIX1 | KIAA0395 | 20q12 |
| ZEB1 | zinc finger E-box binding homeobox 1 | TCF8, PPCD3 | BZP, ZEB, AREB6, NIL-2-A, Zfhep, Zfhx1a | 10p11.22 |
| ZEB2 | zinc finger E-box binding homeobox 2 | ZFHX1B | KIAA0569, SIP-1, SIP1 | 2q22.3 |
| ZEB2P1 | zinc finger E-box binding homeobox 2 pseudogene 1 | ZEB1P1 | 4p15.32 | |
| TSHZ1 | teashirt zinc finger homeobox 1 | SDCCAG33 | NY-CO-33, TSH1 | 18q22.3 |
| TSHZ2 | teashirt zinc finger homeobox 2 | C20orf17, ZNF218 | ZABC2, OVC10-2, TSH2 | 20q13.2 |
| TSHZ3 | teashirt zinc finger homeobox 3 | ZNF537 | KIAA1474, TSH3 | 19q13.11 |
| ADNP | activity-dependent neuroprotector homeobox | KIAA0784, ADNP1 | 20q13.13 | |
| HOMEZ | homeobox and leucine zipper encoding | KIAA1443 | 14q11.2 |
| Approved Symbol | Approved Name | Previous Symbols | Synonyms | Chromosome |
|---|---|---|---|---|
| CERS2 | ceramide synthase 2 | LASS2 | SP260, FLJ10243 | 1q21.3 |
| CERS3 | ceramide synthase 3 | LASS3 | MGC27091 | 15q26.3 |
| CERS4 | ceramide synthase 4 | LASS4 | FLJ12089, Trh1 | 19p13.3 |
| CERS5 | ceramide synthase 5 | LASS5 | Trh4, MGC45411, FLJ25304 | 12q13.12 |
| CERS6 | ceramide synthase 6 | LASS6 | 2q31 |
This online database does not include our confidential data. If you would like to create a new gene symbol and name, the only way to confirm it as unique is by contacting us.




