HGNC ID Approved Symbol Approved Name Status Previous Symbols Synonyms Chromosome Accession Numbers RefSeq IDs Gene Family Tag Gene family description Gene family ID 100 ASIC1 acid sensing ion channel subunit 1 Approved ACCN2 BNaC2, hBNaC2 12q13.12 U78181 NM_020039 ASIC Acid sensing ion channel subunits 290 99 ASIC2 acid sensing ion channel subunit 2 Approved ACCN, ACCN1 ASIC2a, BNC1, BNaC1, hBNaC1, MDEG 17q11.2-q12 AL834182 NM_183377, NM_001094 ASIC Acid sensing ion channel subunits 290 101 ASIC3 acid sensing ion channel subunit 3 Approved ACCN3 TNaC1, DRASIC 7q36.1 AB010575 NM_004769 ASIC Acid sensing ion channel subunits 290 21263 ASIC4 acid sensing ion channel subunit family member 4 Approved ACCN4 BNAC4 2q35 AJ271643 NM_018674 ASIC Acid sensing ion channel subunits 290 17537 ASIC5 acid sensing ion channel subunit family member 5 Approved ACCN5 INAC, HINAC 4q32.1 AJ252011 ASIC Acid sensing ion channel subunits 290 21625 ANO1 anoctamin 1 Approved ORAOV2, TMEM16A TAOS2, FLJ10261, DOG1 11q13.3 BC033036 NM_018043 ANO Anoctamins 865 25519 ANO10 anoctamin 10 Approved TMEM16K FLJ10375, MGC47890, SCAR10 3p22.1-p21.33 AL832508 NM_018075 ANO Anoctamins 865 1183 ANO2 anoctamin 2 Approved C12orf3, TMEM16B 12p13.31 AJ272204 NM_020373 ANO Anoctamins 865 14004 ANO3 anoctamin 3 Approved C11orf25, TMEM16C GENX-3947, DYT23 11p14.2 AJ300461 NM_031418 ANO Anoctamins 865 23837 ANO4 anoctamin 4 Approved TMEM16D FLJ34221, FLJ34272, FLJ35277 12q23.1 AK091540 NM_178826 ANO Anoctamins 865 27337 ANO5 anoctamin 5 Approved TMEM16E, LGMD2L GDD1 11p14.3 AL833271 NM_213599 ANO Anoctamins 865 25240 ANO6 anoctamin 6 Approved TMEM16F DKFZp313M0720 12q12 AL832340 NM_001025356 ANO Anoctamins 865 31677 ANO7 anoctamin 7 Approved PCANAP5, TMEM16G NGEP, PCANAP5L, IPCA-5 2q37.3 AY617079 NM_001001891 ANO Anoctamins 865 29329 ANO8 anoctamin 8 Approved KIAA1623, TMEM16H 19p13.11 AB046843 NM_020959 ANO Anoctamins 865 20679 ANO9 anoctamin 9 Approved TP53I5, TMEM16J PIG5 11p15.5 U33271 NM_001012302 ANO Anoctamins 865 7103 MIP major intrinsic protein of lens fiber Approved MP26, LIM1, AQP0 12q13 NM_012064 AQP Aquaporins 305 633 AQP1 aquaporin 1 (Colton blood group) Approved CO CHIP28 7p14.3 M77829 NM_000385 AQP Aquaporins 305 16029 AQP10 aquaporin 10 Approved 1q21.3 AF159174 NM_080429 AQP Aquaporins 305 19940 AQP11 aquaporin 11 Approved 11q14.1 AB028147 NM_173039 AQP Aquaporins 305 19941 AQP12A aquaporin 12A Approved AQP12 2q37.3 AB040748 NM_198998 AQP Aquaporins 305 6096 AQP12B aquaporin 12B Approved INSSA3 2q37.3 BC041460 AQP Aquaporins 305 634 AQP2 aquaporin 2 Approved 12q13.12 NM_000486 AQP Aquaporins 305 636 AQP3 aquaporin 3 (Gill blood group) Approved GIL 9p13.3 NM_004925 AQP Aquaporins 305 637 AQP4 aquaporin 4 Approved MIWC 18q11.2 U63622 NM_001650, NM_004028 AQP Aquaporins 305 638 AQP5 aquaporin 5 Approved 12q13.12 U46569 NM_001651 AQP Aquaporins 305 639 AQP6 aquaporin 6 Approved AQP2L 12q13.12 AL137716 NM_001652, NM_053286 AQP Aquaporins 305 640 AQP7 aquaporin 7 Approved AQP7L AQP9, AQPap 9p13.3 AB006190 NM_001170 AQP Aquaporins 305 642 AQP8 aquaporin 8 Approved 16p12.1 BC040630 NM_001169 AQP Aquaporins 305 643 AQP9 aquaporin 9 Approved SSC1, HsT17287 15q21.3 AF016495 NM_020980 AQP Aquaporins 305 12703 BEST1 bestrophin 1 Approved VMD2 BMD, BEST, RP50 11q12.3 AF057170 NM_004183 BEST Bestrophins 866 17107 BEST2 bestrophin 2 Approved VMD2L1 FLJ20132 19p13.13 AF440756 NM_017682 BEST Bestrophins 866 17105 BEST3 bestrophin 3 Approved VMD2L3 MGC40411, MGC13168 12q15 AF440758 NM_152439 BEST Bestrophins 866 17106 BEST4 bestrophin 4 Approved VMD2L2 1p34.1 AF440757 NM_153274 BEST Bestrophins 866 1405 CACNG1 calcium voltage-gated channel auxiliary subunit gamma 1 Approved CACNLG 17q24.2 L07738 CACNG Calcium channel auxiliary gamma subunits 1511 1406 CACNG2 calcium voltage-gated channel auxiliary subunit gamma 2 Approved stargazin, MGC138502, MGC138504 22q12.3 AF096322 CACNG Calcium channel auxiliary gamma subunits 1511 1407 CACNG3 calcium voltage-gated channel auxiliary subunit gamma 3 Approved 16p12.1 AF131911 NM_006539 CACNG Calcium channel auxiliary gamma subunits 1511 1408 CACNG4 calcium voltage-gated channel auxiliary subunit gamma 4 Approved MGC11138, MGC24983 17q24.2 AH008289 NM_014405 CACNG Calcium channel auxiliary gamma subunits 1511 1409 CACNG5 calcium voltage-gated channel auxiliary subunit gamma 5 Approved 17q24.2 AF148220 NM_014404, NM_145811 CACNG Calcium channel auxiliary gamma subunits 1511 13625 CACNG6 calcium voltage-gated channel auxiliary subunit gamma 6 Approved 19q13.42 AF288386 CACNG Calcium channel auxiliary gamma subunits 1511 13626 CACNG7 calcium voltage-gated channel auxiliary subunit gamma 7 Approved 19q13.42 AF288387 CACNG Calcium channel auxiliary gamma subunits 1511 13628 CACNG8 calcium voltage-gated channel auxiliary subunit gamma 8 Approved 19q13.42 AF288388 CACNG Calcium channel auxiliary gamma subunits 1511 1388 CACNA1A calcium voltage-gated channel subunit alpha1 A Approved CACNL1A4, SCA6, MHP1, MHP Cav2.1, EA2, APCA, HPCA, FHM 19p13.13 U79666 NM_000068 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1389 CACNA1B calcium voltage-gated channel subunit alpha1 B Approved CACNL1A5 Cav2.2, CACNN 9q34.3 AB209467 NM_000718 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1390 CACNA1C calcium voltage-gated channel subunit alpha1 C Approved CCHL1A1, CACNL1A1 Cav1.2, CACH2, CACN2, TS, LQT8 12p13.33 AF070589 NM_000719 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1391 CACNA1D calcium voltage-gated channel subunit alpha1 D Approved CCHL1A2, CACNL1A2 Cav1.3, CACH3, CACN4 3p21.1 AB209171 NM_000720 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1392 CACNA1E calcium voltage-gated channel subunit alpha1 E Approved CACNL1A6 Cav2.3, BII, CACH6 1q25.3 AK096563 NM_000721 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1393 CACNA1F calcium voltage-gated channel subunit alpha1 F Approved CSNB2, AIED Cav1.4, JM8, JMC8, CSNBX2, CORDX3, CSNB2A, OA2 Xp11.23 AA019975 NM_005183 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1394 CACNA1G calcium voltage-gated channel subunit alpha1 G Approved Cav3.1, NBR13 17q21.33 AC004590 NM_018896 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1395 CACNA1H calcium voltage-gated channel subunit alpha1 H Approved Cav3.2 16p13.3 AL031703 NM_001005407 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1396 CACNA1I calcium voltage-gated channel subunit alpha1 I Approved Cav3.3 22q13.1 AF129133 NM_001003406 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1397 CACNA1S calcium voltage-gated channel subunit alpha1 S Approved HOKPP, MHS5, CACNL1A3 Cav1.1, hypoPP 1q32.1 L33798 NM_000069 CACNA1 Calcium voltage-gated channel alpha1 subunits 1512 1399 CACNA2D1 calcium voltage-gated channel auxiliary subunit alpha2delta 1 Approved CACNL2A, CACNA2, MHS3, LINC01112 lncRNA-N3 7q21.11 M76559 CACNA2D Calcium voltage-gated channel auxiliary alpha2delta subunits 1514 1400 CACNA2D2 calcium voltage-gated channel auxiliary subunit alpha2delta 2 Approved KIAA0558 3p21.31 AF040709 NM_006030 CACNA2D Calcium voltage-gated channel auxiliary alpha2delta subunits 1514 15460 CACNA2D3 calcium voltage-gated channel auxiliary subunit alpha2delta 3 Approved HSA272268 3p21.1-p14.3 AJ272268 CACNA2D Calcium voltage-gated channel auxiliary alpha2delta subunits 1514 20202 CACNA2D4 calcium voltage-gated channel auxiliary subunit alpha2delta 4 Approved 12p13.33 AF516695 CACNA2D Calcium voltage-gated channel auxiliary alpha2delta subunits 1514 1401 CACNB1 calcium voltage-gated channel auxiliary subunit beta 1 Approved CACNLB1 17q12 CACNB Calcium voltage-gated channel auxiliary beta subunits 1515 1402 CACNB2 calcium voltage-gated channel auxiliary subunit beta 2 Approved MYSB, CACNLB2 10p12 U95019 NM_000724 CACNB Calcium voltage-gated channel auxiliary beta subunits 1515 1403 CACNB3 calcium voltage-gated channel auxiliary subunit beta 3 Approved CACNLB3 12q13.12 CACNB Calcium voltage-gated channel auxiliary beta subunits 1515 1404 CACNB4 calcium voltage-gated channel auxiliary subunit beta 4 Approved EJM4 2q23.3 AF038852 NM_000726.3 CACNB Calcium voltage-gated channel auxiliary beta subunits 1515 17116 CATSPER1 cation channel sperm associated 1 Approved CATSPER 11q13.1 AF407333 NM_053054 CATSPER Cation channels sperm associated 186 18810 CATSPER2 cation channel sperm associated 2 Approved 15q15.3 AF411817 NM_054020 CATSPER Cation channels sperm associated 186 20819 CATSPER3 cation channel sperm associated 3 Approved CACRC 5q31.1 AF432876 NM_178019 CATSPER Cation channels sperm associated 186 23220 CATSPER4 cation channel sperm associated 4 Approved 1p36.11 BN000273 NM_198137 CATSPER Cation channels sperm associated 186 20500 CATSPERB cation channel sperm associated auxiliary subunit beta Approved C14orf161 FLJ14298 14q32.12 AK024360 NM_024764 CATSPER Cation channels sperm associated 186 28598 CATSPERD cation channel sperm associated auxiliary subunit delta Approved TMEM146 MGC39581 19p13.3 BC043005 NM_152784 CATSPER Cation channels sperm associated 186 25243 CATSPERG cation channel sperm associated auxiliary subunit gamma Approved C19orf15 DKFZp434A1022, FLJ46353 19q13.2 AK128220 NM_021185 CATSPER Cation channels sperm associated 186 1884 CFTR cystic fibrosis transmembrane conductance regulator Approved CF, ABCC7 MRP7, ABC35, TNR-CFTR, dJ760C5.1, CFTR/MRP 7q31.2 M28668 NM_000492 CFTR Chloride channels, ATP-gated CFTR 309 2062 CLIC1 chloride intracellular channel 1 Approved NCC27, p64CLCP, G6 6p21.33 U93205 NM_001288 CLIC Chloride intracellular channels 307 2063 CLIC2 chloride intracellular channel 2 Approved XAP121 Xq28 AJ000217 NM_001289 CLIC Chloride intracellular channels 307 2064 CLIC3 chloride intracellular channel 3 Approved 9q34.3 AF102166 NM_004669 CLIC Chloride intracellular channels 307 13518 CLIC4 chloride intracellular channel 4 Approved DKFZP566G223, CLIC4L, P64H1, H1, huH1, p64H1 1p36.11 AF097330 NM_013943 CLIC Chloride intracellular channels 307 13517 CLIC5 chloride intracellular channel 5 Approved DFNB102 6p21.1 AF216941 CLIC Chloride intracellular channels 307 2065 CLIC6 chloride intracellular channel 6 Approved CLIC1L CLIC5 21q22.12 AF426169 CLIC Chloride intracellular channels 307 2019 CLCN1 chloride voltage-gated channel 1 Approved CLC1, ClC-1 7q34 Z25884 NM_000083 CLCN Chloride voltage-gated channels 302 2020 CLCN2 chloride voltage-gated channel 2 Approved CLC2, EJM6, ClC-2 3q27.1 S77770 CLCN Chloride voltage-gated channels 302 2021 CLCN3 chloride voltage-gated channel 3 Approved CLC3, ClC-3 4q33 X78520 CLCN Chloride voltage-gated channels 302 2022 CLCN4 chloride voltage-gated channel 4 Approved CLC4, ClC-4 Xp22.2 X77197 CLCN Chloride voltage-gated channels 302 2023 CLCN5 chloride voltage-gated channel 5 Approved NPHL2, NPHL1 DENTS, XLRH, hClC-K2, hCIC-K2, CLC5, XRN, ClC-5 Xp11.23 X91906 CLCN Chloride voltage-gated channels 302 2024 CLCN6 chloride voltage-gated channel 6 Approved CLC-6, KIAA0046, ClC-6 1p36.22 X83378 NM_001286 CLCN Chloride voltage-gated channels 302 2025 CLCN7 chloride voltage-gated channel 7 Approved CLC-7, OPTA2, CLC7, ClC-7, PPP1R63 16p13.3 Z67743 NM_001287 CLCN Chloride voltage-gated channels 302 2026 CLCNKA chloride voltage-gated channel Ka Approved hClC-Ka 1p36.13 CLCN Chloride voltage-gated channels 302 2027 CLCNKB chloride voltage-gated channel Kb Approved hClC-Kb 1p36.13 AK098217 NM_000085 CLCN Chloride voltage-gated channels 302 16512 BSND barttin CLCNK type accessory beta subunit Approved DFNB73 BART 1p32.3 AY034632 NM_057176 CLCN Chloride voltage-gated channels 302 4274 GJA1 gap junction protein alpha 1 Approved ODDD, GJAL CX43, ODD, ODOD, SDTY3 6q22.31 BC026329 NM_000165 GJ Gap junction proteins 314 16995 GJA10 gap junction protein alpha 10 Approved CX62 6q15 AF296766 NM_032602 GJ Gap junction proteins 314 4277 GJA3 gap junction protein alpha 3 Approved CZP3 CX46 13q12.11 AF075290 NM_021954 GJ Gap junction proteins 314 4278 GJA4 gap junction protein alpha 4 Approved CX37 1p34.3 M96789 NM_002060 GJ Gap junction proteins 314 4279 GJA5 gap junction protein alpha 5 Approved CX40 1q21.2 NM_181703 GJ Gap junction proteins 314 32542 GJA6P gap junction protein alpha 6 pseudogene Approved Xp22.13 GJ Gap junction proteins 314 4281 GJA8 gap junction protein alpha 8 Approved CAE1, CZP1, CAE CX50 1q21.2 U34802 NM_005267 GJ Gap junction proteins 314 19155 GJA9 gap junction protein alpha 9 Approved GJA10 CX59, CX58 1p34.3 AF179597 NM_030772 GJ Gap junction proteins 314 4283 GJB1 gap junction protein beta 1 Approved CMTX1, CMTX CX32 Xq13.1 X04325 NM_000166 GJ Gap junction proteins 314 4284 GJB2 gap junction protein beta 2 Approved DFNB1, DFNA3 CX26, NSRD1 13q12.11 M86849 GJ Gap junction proteins 314 4285 GJB3 gap junction protein beta 3 Approved DFNA2, EKV CX31 1p34.3 BC012918 NM_024009 GJ Gap junction proteins 314 4286 GJB4 gap junction protein beta 4 Approved CX30.3 1p34.3 NM_153212 GJ Gap junction proteins 314 4287 GJB5 gap junction protein beta 5 Approved CX31.1 1p34.3 BC004379 NM_005268 GJ Gap junction proteins 314 4288 GJB6 gap junction protein beta 6 Approved DFNA3, ED2 EDH, HED, CX30 13q12.11 AJ005585 GJ Gap junction proteins 314 16690 GJB7 gap junction protein beta 7 Approved CX25, bA136M9.1 6q14.3-q15 AJ414563 GJ Gap junction proteins 314 4280 GJC1 gap junction protein gamma 1 Approved GJA7 CX45 17q21.31 U03493 NM_005497 GJ Gap junction proteins 314 17494 GJC2 gap junction protein gamma 2 Approved GJA12 CX47, CX46.6, SPG44 1q42.13 AF014643 NM_020435 GJ Gap junction proteins 314 17495 GJC3 gap junction protein gamma 3 Approved GJE1 CX30.2 7q22.1 AF503615 NM_181538 GJ Gap junction proteins 314 19154 GJD2 gap junction protein delta 2 Approved GJA9 CX36 15q14 AB037509 GJ Gap junction proteins 314 19147 GJD3 gap junction protein delta 3 Approved GJC1 CX31.9, GJA11, Cx30.2 17q21.2 AF514298 NM_152219 GJ Gap junction proteins 314 23296 GJD4 gap junction protein delta 4 Approved CX40.1, FLJ90023 10p11.21 AJ414564 NM_153368 GJ Gap junction proteins 314 33251 GJE1 gap junction protein epsilon 1 Approved CX23 6q24.1 GJ Gap junction proteins 314 6180 ITPR1 inositol 1,4,5-trisphosphate receptor type 1 Approved SCA15, SCA16, SCA29 Insp3r1, IP3R1, ACV, PPP1R94 3p26.1 D26070 NM_002222 ITPR Inositol 1,4,5-triphosphate receptors 297 6181 ITPR2 inositol 1,4,5-trisphosphate receptor type 2 Approved IP3R2, CFAP48 12p11.23 D26350 NM_002223 ITPR Inositol 1,4,5-triphosphate receptors 297 6182 ITPR3 inositol 1,4,5-trisphosphate receptor type 3 Approved IP3R3 6p21.31 D26351 NM_002224 ITPR Inositol 1,4,5-triphosphate receptors 297 6284 KCNMA1 potassium calcium-activated channel subfamily M alpha 1 Approved SLO KCa1.1, mSLO1 10q22.3 U11717 NM_002247 Potassium calcium-activated channels 255 6290 KCNN1 potassium calcium-activated channel subfamily N member 1 Approved KCa2.1, hSK1 19p13.11 U69883 NM_002248 Potassium calcium-activated channels 255 6291 KCNN2 potassium calcium-activated channel subfamily N member 2 Approved KCa2.2, hSK2 5q22.3 AF239613 NM_021614 Potassium calcium-activated channels 255 6292 KCNN3 potassium calcium-activated channel subfamily N member 3 Approved KCa2.3, hSK3, SKCA3 1q21.3 AF031815 NM_002249 Potassium calcium-activated channels 255 6293 KCNN4 potassium calcium-activated channel subfamily N member 4 Approved KCa3.1, hSK4, hKCa4, hIKCa1, IK 19q13.31 AF022797 NM_002250 Potassium calcium-activated channels 255 18867 KCNU1 potassium calcium-activated channel subfamily U member 1 Approved KCa5.1, Slo3, KCNMC1, Kcnma3 8p11.23 BC028701 NM_001031836 Potassium calcium-activated channels 255 18865 KCNT1 potassium sodium-activated channel subfamily T member 1 Approved KCa4.1, KIAA1422, SLACK, Slo2.2 9q34.3 AB037843 NM_020822 KCNT Potassium sodium-activated channel subfamily T 856 18866 KCNT2 potassium sodium-activated channel subfamily T member 2 Approved KCa4.2, SLICK, SLO2.1 1q31.3 BX647852, AY359444, AK127807 NM_198503 KCNT Potassium sodium-activated channel subfamily T 856 6272 KCNK1 potassium two pore domain channel subfamily K member 1 Approved K2p1.1, DPK, TWIK-1 1q42.2 U33632 NM_002245 KCNK Potassium two pore domain channel subfamily K 277 6273 KCNK10 potassium two pore domain channel subfamily K member 10 Approved K2p10.1, TREK-2, TREK2, PPP1R97 14q31.3 AF279890 NM_021161 KCNK Potassium two pore domain channel subfamily K 277 6274 KCNK12 potassium two pore domain channel subfamily K member 12 Approved THIK-2, THIK2, K2p12.1 2p16.3 AF287302 NM_022055 KCNK Potassium two pore domain channel subfamily K 277 6275 KCNK13 potassium two pore domain channel subfamily K member 13 Approved K2p13.1, THIK-1, THIK1 14q32.11 AF287303 NM_022054 KCNK Potassium two pore domain channel subfamily K 277 13814 KCNK15 potassium two pore domain channel subfamily K member 15 Approved KCNK11, KCNK14 K2p15.1, dJ781B1.1, KT3.3, KIAA0237, TASK5, TASK-5 20q13.12 AF257081 NM_022358 KCNK Potassium two pore domain channel subfamily K 277 14464 KCNK16 potassium two pore domain channel subfamily K member 16 Approved K2p16.1, TALK-1, TALK1 6p21.2 AF358909 NM_032115 KCNK Potassium two pore domain channel subfamily K 277 14465 KCNK17 potassium two pore domain channel subfamily K member 17 Approved K2p17.1, TALK-2, TALK2, TASK4, TASK-4 6p21.2 AF358910 NM_031460 KCNK Potassium two pore domain channel subfamily K 277 19439 KCNK18 potassium two pore domain channel subfamily K member 18 Approved K2p18.1, TRESK-2, TRESK2, TRESK, TRIK 10q25.3 AB087138 NM_181840 KCNK Potassium two pore domain channel subfamily K 277 6277 KCNK2 potassium two pore domain channel subfamily K member 2 Approved K2p2.1, TREK-1 1q41 AF004711 NM_014217 KCNK Potassium two pore domain channel subfamily K 277 6278 KCNK3 potassium two pore domain channel subfamily K member 3 Approved K2p3.1, TASK, TASK-1 2p23.3 AF006823 NM_002246 KCNK Potassium two pore domain channel subfamily K 277 6279 KCNK4 potassium two pore domain channel subfamily K member 4 Approved K2p4.1, TRAAK 11q13.1 AF247042 NM_033311 KCNK Potassium two pore domain channel subfamily K 277 6280 KCNK5 potassium two pore domain channel subfamily K member 5 Approved K2p5.1, TASK-2 6p21.2 AF084830 NM_003740 KCNK Potassium two pore domain channel subfamily K 277 6281 KCNK6 potassium two pore domain channel subfamily K member 6 Approved K2p6.1, TWIK-2 19q13.2 AF117708 NM_004823 KCNK Potassium two pore domain channel subfamily K 277 6282 KCNK7 potassium two pore domain channel subfamily K member 7 Approved K2p7.1 11q13.1 AF110522 NM_005714 KCNK Potassium two pore domain channel subfamily K 277 6283 KCNK9 potassium two pore domain channel subfamily K member 9 Approved K2p9.1, TASK3, TASK-3 8q24.3 AF212829 NM_016601 KCNK Potassium two pore domain channel subfamily K 277 6255 KCNJ1 potassium voltage-gated channel subfamily J member 1 Approved Kir1.1, ROMK1 11q24.3 BC063109 NM_000220 KCNJ Potassium voltage-gated channel subfamily J 276 6256 KCNJ10 potassium voltage-gated channel subfamily J member 10 Approved Kir4.1, Kir1.2 1q23.2 U52155 NM_002241 KCNJ Potassium voltage-gated channel subfamily J 276 6257 KCNJ11 potassium voltage-gated channel subfamily J member 11 Approved Kir6.2, BIR 11p15.1 D50582 NM_000525 KCNJ Potassium voltage-gated channel subfamily J 276 6258 KCNJ12 potassium voltage-gated channel subfamily J member 12 Approved KCNJN1 Kir2.2, Kir2.2v, IRK2, hIRK1 17p11.2 L36069 NM_021012 KCNJ Potassium voltage-gated channel subfamily J 276 6259 KCNJ13 potassium voltage-gated channel subfamily J member 13 Approved Kir7.1, Kir1.4, LCA16 2q37.1 AJ006128 NM_002242 KCNJ Potassium voltage-gated channel subfamily J 276 6260 KCNJ14 potassium voltage-gated channel subfamily J member 14 Approved Kir2.4, IRK4 19q13.33 BC042033 NM_013348 KCNJ Potassium voltage-gated channel subfamily J 276 6261 KCNJ15 potassium voltage-gated channel subfamily J member 15 Approved Kir4.2, Kir1.3, IRKK 21q22.13-q22.2 Y10745 NM_002243 KCNJ Potassium voltage-gated channel subfamily J 276 6262 KCNJ16 potassium voltage-gated channel subfamily J member 16 Approved Kir5.1, BIR9 17q24.3 AF153815 NM_018658 KCNJ Potassium voltage-gated channel subfamily J 276 39080 KCNJ18 potassium voltage-gated channel subfamily J member 18 Approved KIR2.6, TTPP2 17p11.2 NM_001194958 KCNJ Potassium voltage-gated channel subfamily J 276 6263 KCNJ2 potassium voltage-gated channel subfamily J member 2 Approved Kir2.1, IRK1, LQT7 17q24.3 AF011904 NM_000891 KCNJ Potassium voltage-gated channel subfamily J 276 6264 KCNJ3 potassium voltage-gated channel subfamily J member 3 Approved Kir3.1, GIRK1, KGA 2q24.1 U50964 NM_002239 KCNJ Potassium voltage-gated channel subfamily J 276 6265 KCNJ4 potassium voltage-gated channel subfamily J member 4 Approved Kir2.3, HIR, HRK1, hIRK2, IRK3 22q13.1 U07364 NM_004981 KCNJ Potassium voltage-gated channel subfamily J 276 6266 KCNJ5 potassium voltage-gated channel subfamily J member 5 Approved Kir3.4, CIR, KATP1, GIRK4, LQT13 11q24.3 D50134 NM_000890 KCNJ Potassium voltage-gated channel subfamily J 276 6267 KCNJ6 potassium voltage-gated channel subfamily J member 6 Approved KCNJ7 Kir3.2, GIRK2, KATP2, BIR1, hiGIRK2 21q22.13 U24660 NM_002240 KCNJ Potassium voltage-gated channel subfamily J 276 6269 KCNJ8 potassium voltage-gated channel subfamily J member 8 Approved Kir6.1 12p12.1 BC000544 NM_004982 KCNJ Potassium voltage-gated channel subfamily J 276 6270 KCNJ9 potassium voltage-gated channel subfamily J member 9 Approved Kir3.3, GIRK3 1q23.2 U52152 NM_004983 KCNJ Potassium voltage-gated channel subfamily J 276 6218 KCNA1 potassium voltage-gated channel subfamily A member 1 Approved AEMK Kv1.1, RBK1, HUK1, MBK1 12p13.32 L02750 NM_000217 Potassium voltage-gated channels 274 6219 KCNA10 potassium voltage-gated channel subfamily A member 10 Approved Kv1.8 1p13.3 U96110 NM_005549 Potassium voltage-gated channels 274 6220 KCNA2 potassium voltage-gated channel subfamily A member 2 Approved Kv1.2, HK4 1p13.3 L02752 NM_004974 Potassium voltage-gated channels 274 6221 KCNA3 potassium voltage-gated channel subfamily A member 3 Approved Kv1.3, MK3, HLK3, HPCN3 1p13.3 L23499 NM_002232 Potassium voltage-gated channels 274 6222 KCNA4 potassium voltage-gated channel subfamily A member 4 Approved KCNA4L Kv1.4, HK1, HPCN2 11p14.1 M55514 NM_002233 Potassium voltage-gated channels 274 6224 KCNA5 potassium voltage-gated channel subfamily A member 5 Approved Kv1.5, HK2, HPCN1 12p13.32 M83254 NM_002234 Potassium voltage-gated channels 274 6225 KCNA6 potassium voltage-gated channel subfamily A member 6 Approved Kv1.6, HBK2, PPP1R96 12p13 X17622 NM_002235 Potassium voltage-gated channels 274 6226 KCNA7 potassium voltage-gated channel subfamily A member 7 Approved Kv1.7, HAK6 19q13.33 AF315818 NM_031886 Potassium voltage-gated channels 274 6231 KCNB1 potassium voltage-gated channel subfamily B member 1 Approved Kv2.1 20q13.13 AF026005 NM_004975 Potassium voltage-gated channels 274 6232 KCNB2 potassium voltage-gated channel subfamily B member 2 Approved Kv2.2 8q21.11 U69962 NM_004770 Potassium voltage-gated channels 274 6233 KCNC1 potassium voltage-gated channel subfamily C member 1 Approved Kv3.1 11p15.1 M96747 NM_004976 Potassium voltage-gated channels 274 6234 KCNC2 potassium voltage-gated channel subfamily C member 2 Approved Kv3.2 12q21.1 AF268896 NM_153748 Potassium voltage-gated channels 274 6235 KCNC3 potassium voltage-gated channel subfamily C member 3 Approved SCA13 Kv3.3 19q13.33 AB208930 NM_004977 Potassium voltage-gated channels 274 6236 KCNC4 potassium voltage-gated channel subfamily C member 4 Approved C1orf30 Kv3.4, HKSHIIIC 1p13.3 BC101769 NM_001039574 Potassium voltage-gated channels 274 6237 KCND1 potassium voltage-gated channel subfamily D member 1 Approved Kv4.1 Xp11.23 AF166003 NM_004979 Potassium voltage-gated channels 274 6238 KCND2 potassium voltage-gated channel subfamily D member 2 Approved Kv4.2, RK5, KIAA1044 7q31.31 AJ010969 NM_012281 Potassium voltage-gated channels 274 6239 KCND3 potassium voltage-gated channel subfamily D member 3 Approved SCA22, SCA19 Kv4.3, KSHIVB 1p13.2 AF048713 NM_172198 Potassium voltage-gated channels 274 6246 KCNF1 potassium voltage-gated channel modifier subfamily F member 1 Approved KCNF Kv5.1, kH1, IK8 2p25.1 AF033382 NM_002236 Potassium voltage-gated channels 274 6248 KCNG1 potassium voltage-gated channel modifier subfamily G member 1 Approved KCNG Kv6.1, kH2, K13 20q13.13 AF033383 NM_002237 Potassium voltage-gated channels 274 6249 KCNG2 potassium voltage-gated channel modifier subfamily G member 2 Approved Kv6.2, KCNF2 18q23 AJ011021 NM_012283 Potassium voltage-gated channels 274 18306 KCNG3 potassium voltage-gated channel modifier subfamily G member 3 Approved Kv6.3 2p21 AB070604 NM_172344 Potassium voltage-gated channels 274 19697 KCNG4 potassium voltage-gated channel modifier subfamily G member 4 Approved Kv6.4 16q24.1 AF348984 NM_172347 Potassium voltage-gated channels 274 6250 KCNH1 potassium voltage-gated channel subfamily H member 1 Approved Kv10.1, eag, h-eag, eag1 1q32.2 AJ001366 NM_002238 Potassium voltage-gated channels 274 6251 KCNH2 potassium voltage-gated channel subfamily H member 2 Approved LQT2 Kv11.1, HERG, erg1 7q36.1 U04270 NM_000238 Potassium voltage-gated channels 274 6252 KCNH3 potassium voltage-gated channel subfamily H member 3 Approved Kv12.2, BEC1, elk2 12q13.12 AB022696 NM_012284 Potassium voltage-gated channels 274 6253 KCNH4 potassium voltage-gated channel subfamily H member 4 Approved Kv12.3, elk1 17q21.2 AB022698 NM_012285 Potassium voltage-gated channels 274 6254 KCNH5 potassium voltage-gated channel subfamily H member 5 Approved Kv10.2, H-EAG2, eag2 14q23.2 U69185 NM_139318 Potassium voltage-gated channels 274 18862 KCNH6 potassium voltage-gated channel subfamily H member 6 Approved Kv11.2, erg2, HERG2 17q23.3 AF311913 NM_030779 Potassium voltage-gated channels 274 18863 KCNH7 potassium voltage-gated channel subfamily H member 7 Approved Kv11.3, HERG3, erg3 2q24.2 AF032897 NM_033272 Potassium voltage-gated channels 274 18864 KCNH8 potassium voltage-gated channel subfamily H member 8 Approved Kv12.1, elk3 3p24.3 AY053503 NM_144633 Potassium voltage-gated channels 274 6294 KCNQ1 potassium voltage-gated channel subfamily Q member 1 Approved LQT, KCNA9 Kv7.1, KCNA8, KVLQT1, JLNS1, LQT1 11p15.5-p15.4 AF000571 NM_000218 Potassium voltage-gated channels 274 6296 KCNQ2 potassium voltage-gated channel subfamily Q member 2 Approved EBN, EBN1 Kv7.2, ENB1, BFNC, KCNA11, HNSPC 20q13.33 AF033348 NM_172109 Potassium voltage-gated channels 274 6297 KCNQ3 potassium voltage-gated channel subfamily Q member 3 Approved EBN2 Kv7.3 8q24.22 AB208890 NM_004519 Potassium voltage-gated channels 274 6298 KCNQ4 potassium voltage-gated channel subfamily Q member 4 Approved DFNA2 Kv7.4 1p34.2 AF105202 NM_004700 Potassium voltage-gated channels 274 6299 KCNQ5 potassium voltage-gated channel subfamily Q member 5 Approved Kv7.5 6q13 AF202977 NM_019842 Potassium voltage-gated channels 274 6300 KCNS1 potassium voltage-gated channel modifier subfamily S member 1 Approved Kv9.1 20q13.12 AF043473 NM_002251 Potassium voltage-gated channels 274 6301 KCNS2 potassium voltage-gated channel modifier subfamily S member 2 Approved Kv9.2 8q22.2 AB032970 NM_020697 Potassium voltage-gated channels 274 6302 KCNS3 potassium voltage-gated channel modifier subfamily S member 3 Approved Kv9.3 2p24.2 AF043472 NM_002252 Potassium voltage-gated channels 274 18861 KCNV1 potassium voltage-gated channel modifier subfamily V member 1 Approved Kv8.1 8q23.2 AF167082 NM_014379 Potassium voltage-gated channels 274 19698 KCNV2 potassium voltage-gated channel modifier subfamily V member 2 Approved Kv8.2 9p24.2 AF348983 NM_133497 Potassium voltage-gated channels 274 10483 RYR1 ryanodine receptor 1 Approved MHS, MHS1, CCO RYR, PPP1R137 19q13.2 J05200 RYR Ryanodine receptors 287 10484 RYR2 ryanodine receptor 2 Approved ARVD2 ARVC2, VTSIP 1q43 X91869 NM_001035 RYR Ryanodine receptors 287 10485 RYR3 ryanodine receptor 3 Approved 15q13.3-q14 RYR Ryanodine receptors 287 10599 SCNN1A sodium channel epithelial 1 alpha subunit Approved SCNN1 ENaCalpha 12p13 Z92978 SCNN Sodium channels epithelial 185 10600 SCNN1B sodium channel epithelial 1 beta subunit Approved ENaCbeta 16p12.2-p12.1 X87159 SCNN Sodium channels epithelial 185 10601 SCNN1D sodium channel epithelial 1 delta subunit Approved ENaCdelta, dNaCh 1p36.33 U38254 NM_002978 SCNN Sodium channels epithelial 185 10602 SCNN1G sodium channel epithelial 1 gamma subunit Approved ENaCgamma, SCNEG 16p12.2 U48937 NM_001039 SCNN Sodium channels epithelial 185 19082 NALCN sodium leak channel, non-selective Approved VGCNL1 bA430M15.1, CanIon 13q32.3-q33.1 AY141972 NM_052867 NALCN Sodium leak channels, non selective 283 10582 SCN10A sodium voltage-gated channel alpha subunit 10 Approved Nav1.8, hPN3, SNS, PN3 3p22.2 AF117907 NM_006514 Sodium voltage-gated channel alpha subunits 1203 10583 SCN11A sodium voltage-gated channel alpha subunit 11 Approved SCN12A Nav1.9, NaN, SNS-2 3p22.2 AF126739 NM_014139 Sodium voltage-gated channel alpha subunits 1203 10585 SCN1A sodium voltage-gated channel alpha subunit 1 Approved SCN1, FEB3 Nav1.1, GEFSP2, HBSCI, NAC1, SMEI 2q24.3 AB093548 NM_006920 Sodium voltage-gated channel alpha subunits 1203 10588 SCN2A sodium voltage-gated channel alpha subunit 2 Approved SCN2A1, SCN2A2 Nav1.2, HBSCII, HBSCI 2q24.3 AB208888 NM_021007 Sodium voltage-gated channel alpha subunits 1203 10590 SCN3A sodium voltage-gated channel alpha subunit 3 Approved Nav1.3 2q24.3 AF035685 NM_006922 Sodium voltage-gated channel alpha subunits 1203 10591 SCN4A sodium voltage-gated channel alpha subunit 4 Approved HYKPP Nav1.4, HYPP, SkM1 17q23.3 U24693 NM_000334 Sodium voltage-gated channel alpha subunits 1203 10593 SCN5A sodium voltage-gated channel alpha subunit 5 Approved CMD1E Nav1.5, LQT3, HB1, HBBD, PFHB1, IVF, HB2, HH1, SSS1, CDCD2, CMPD2, ICCD 3p22.2 AJ310893 NM_198056 Sodium voltage-gated channel alpha subunits 1203 10596 SCN8A sodium voltage-gated channel alpha subunit 8 Approved MED Nav1.6, NaCh6, PN4, CerIII, CIAT 12q13.13 AB027567 NM_014191 Sodium voltage-gated channel alpha subunits 1203 10597 SCN9A sodium voltage-gated channel alpha subunit 9 Approved Nav1.7, PN1, NE-NA, NENA, ETHA 2q24.3 X82835 NM_002977 Sodium voltage-gated channel alpha subunits 1203 10586 SCN1B sodium voltage-gated channel beta subunit 1 Approved 19q13.11 Sodium voltage-gated channel beta subunits 1204 10589 SCN2B sodium voltage-gated channel beta subunit 2 Approved 11q23.3 AY358945 NM_004588 Sodium voltage-gated channel beta subunits 1204 20665 SCN3B sodium voltage-gated channel beta subunit 3 Approved HSA243396 11q24.1 AJ243396 NM_018400 Sodium voltage-gated channel beta subunits 1204 10592 SCN4B sodium voltage-gated channel beta subunit 4 Approved LQT10 11q23.3 AY149967 Sodium voltage-gated channel beta subunits 1204 18182 TPCN1 two pore segment channel 1 Approved KIAA1169, FLJ20612, TPC1 12q24.13 AB032995 NM_017901 TPCN Two pore segment channels 247 20820 TPCN2 two pore segment channel 2 Approved TPC2 11q13.3 AK023366 NM_139075 TPCN Two pore segment channels 247 12669 VDAC1 voltage dependent anion channel 1 Approved MGC111064, PORIN 5q31.1 VDAC Voltage dependent anion channels 306 12672 VDAC2 voltage dependent anion channel 2 Approved 10q22.2 BC000165 NM_003375 VDAC Voltage dependent anion channels 306 12674 VDAC3 voltage dependent anion channel 3 Approved HD-VDAC3 8p11.21 AF038962 VDAC Voltage dependent anion channels 306